Clinical-radiological correlation as the first route in the diagnosis of Gorham-Stout syndrome

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DOI:

https://doi.org/10.21615/cesmedicina.34.3.4

Keywords:

Osteolysis, Spontaneous fractures, Rare diseases, Gorham-Stout syndrome

Abstract

Gorham-Stout syndrome is a rare bone disease whose etiology remains unknown, characterized by osteolysis and abnormal proliferation of vascular
channels. We describe the case of a 47-year-old male patient who consulted for 15 days of evolution of edema, pain, erythema and seroma expulsion from surgical wound in the right shoulder, with a recent diagnosis of septic arthritis. He referred a history of Gorham-Stout syndrome, evidenced with physic al examination and comparative radiography of the shoulders. The clinical presentation of these patients depends on the affected area and the extent of the disease, making their diagnosis a challenge in case the deterioration occurs in unexposed areas. The main symptom is localized pain, accompanied by swelling, weakness and functional impairment of the affected limbs. These patients may remain asymptomatic until suffering a bone fracture spontaneously or after minor trauma. 

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References

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A City Park (c. 1887) William Merritt Chase. Estados Unidos, 1849–1916 Art Institute Chicago

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Published

2020-12-09

How to Cite

Lozada Martinez, I. D., Llamas Nieves, A., Bolaño Romero, M., & Herrera Lomonaco, S. (2020). Clinical-radiological correlation as the first route in the diagnosis of Gorham-Stout syndrome. CES Medicina, 34(3), 207–214. https://doi.org/10.21615/cesmedicina.34.3.4

Issue

Vol. 34 No. 3 (2020): CES Medicina

Section

Reporte de caso

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